Familial renal amyloidosis
id:
familial-renal-amyloidosis-274-13265982
title:
Familial renal amyloidosis
text:
Familial renal amyloidosis is a form of amyloidosis primarily presenting in the kidney. It is associated most commonly with congenital mutations in the fibrinogen alpha chain and classified as a dysfibrinogenemia. and, less commonly, with congenital mutations in apolipoprotein A1 and lysozyme. It is also known as "Ostertag" type, after B. Ostertag, who characterized it in 1932 and 1950.
brand slug:
wiki
category slug:
encyclopedia
description:
Medical condition
original url:
https://en.wikipedia.org/wiki/Familial_renal_amyloidosis
date created:
date modified:
2024-02-15T12:46:58Z
main entity:
{"identifier":"Q13581332","url":"https://www.wikidata.org/entity/Q13581332"}
image:
{"content_url":"https://upload.wikimedia.org/wikipedia/commons/4/4e/Autosomal_dominant_-_en.svg","width":738,"height":1260}
fields total:
13
integrity:
15