Carnitine-acylcarnitine translocase deficiency

id: carnitine-acylcarnitine-translocase-deficiency-319-14232019
title: Carnitine-acylcarnitine translocase deficiency
text: Carnitine-acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long-chain fatty acids into energy, particularly during periods without food. Carnitine, a natural substance acquired mostly through the diet, is used by cells to process fats and produce energy. People with this disorder have a faulty enzyme that prevents long-chain fatty acids from being transported into the innermost part of the mitochondria for processing.
brand slug: wiki
category slug: encyclopedia
description: Medical condition
original url: https://en.wikipedia.org/wiki/Carnitine-acylcarnitine_translocase_deficiency
date created:
date modified: 2023-09-14T13:42:46Z
main entity: {"identifier":"Q5044061","url":"https://www.wikidata.org/entity/Q5044061"}
image: {"content_url":"https://upload.wikimedia.org/wikipedia/commons/3/3e/Autorecessive.svg","width":1350,"height":1580}
fields total: 13
integrity: 15

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