Agammaglobulinemia-microcephaly-craniosynostosis-severe dermatitis syndrome

id: agammaglobulinemia-microcephaly-craniosynostosis-severe-dermatitis-syndrome-251-7903938
title: Agammaglobulinemia-microcephaly-craniosynostosis-severe dermatitis syndrome
text: Agammaglobulinemia-microcephaly-craniosynostosis-severe dermatitis syndrome is a rare autosomal recessive syndromic form of agammaglobulinemia that is caused by profound B-cell depletion with normal T-cell numbers. The condition was first identified in a 2006 report.
brand slug: wiki
category slug: encyclopedia
description: Medical condition
original url: https://en.wikipedia.org/wiki/Agammaglobulinemia-microcephaly-craniosynostosis-severe_dermatitis_syndrome
date created:
date modified: 2024-04-15T06:32:53Z
main entity: {"identifier":"Q55783750","url":"https://www.wikidata.org/entity/Q55783750"}
image: {"content_url":"https://upload.wikimedia.org/wikipedia/commons/a/a4/Autorecessive.jpg","width":307,"height":396}
fields total: 13
integrity: 15

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